1)bullosa表皮松解症
1.Hallopeau-Siemens type of recessive dystrophic epidermolysis bullosa: a case report;常染色体隐性遗传的Hallopeau-Siemens型营养不良型大疱性表皮松解症1例
英文短句/例句
1.epidermolysis bullosa acquisita, EBA获得性大疱性表皮松解症
2.Laboratory Diagnoses of Epidermolysis Bullosa Acquisita;获得性大疱性表皮松解症的实验诊断
3.A case of recessive dystrophic epidermolysis bullosa隐性遗传营养不良型大疱性表皮松解症1例
4.Toxic bullosa epidermalysis associated with metamizole sodium tablets安乃近片相关中毒性大疱性表皮松解症
5.Dominant Dystrophic Epidermolysis Bullosa: Mutation Analysis;显性营养不良型大疱性表皮松解症的基因突变研究
6.Study on Gene Mutation of Two Dystrophic Epidermolysis Bullosa Pedigrees;两营养不良型大疱表皮松解症家系基因突变的研究
7.The Report of One Clan with Dystrophic Epidermolysis Bullosa Dominant;遗传性营养不良型大疱性表皮松解症一家系报告
8.Mutation Analysis of COL7A1 Gene in Two Chinese Families with Dystrophic Epidermolysis Bullosa Pruriginosa;痒疹样营养不良型大疱性表皮松解症两家系基因突变分析
9.Family Survey of Clinicopathologic Characteristics of Dystrophic Epidermolysis Bullosa Pruriginosa痒疹样营养不良型大疱性表皮松解症两家系调查
10.A Recurrent Keratin 14 Mutation in Dowling-Mearaepidermolysis Bullosa Simplex单纯型大疱性表皮松解症Dowling-Meara亚型基因突变检测
11.Treatment for dystrophic epidermolysis bullosa using tissue-engineering technique and cell therapy组织工程技术和细胞疗法治疗营养不良性大疱性表皮松解症
12.A family report of albopapuloid epidermolysis bullosa dystrophica dominant白色丘疹样显性营养不良型大疱性表皮松解症一家系报告
13.Dystrophic Epidermolysis Bullosa: Analysis of Clinical and Genetic Features and Study on the Structure Deficiency of Basement Membrane Zone;营养不良型大疱性表皮松解症：临床、遗传特点分析及其基底膜带结构缺陷的研究
14.Restoration of Recombinant Human Type VII Collagen and Correction of the Disease Phenotype in a Murine Model of Dystrophic Epidermolysis Bullosa;重组人VII型胶原蛋白对营养不良性大疱性表皮松解症治疗作用的实验研究
15.Mutation Analysis of KRT9 Gene in a Chinese Family with Epidermolytic Palmoplantar Keratoderma;表皮松解性掌跖角化症一家系的基因突变研究
16.Nursing of Bullous Epidermal Necrolysis Induced by Trichloroethylene三氯乙烯致大疱表皮坏死松解症的护理
17.Analysis of 18 cases of major erythema multiforme and toxic epidermal necrolysis重症多形红斑及中毒性表皮坏死松解症18例临床分析
18.hyperplastic epidermolysis bullosa增生性大疱性表皮松解
相关短句/例句
Epidermal Necrolysis表皮坏死松解症
1.Clinical analysis of 40 cases of drug-induced toxic epidermal necrolysis/Stevens-Johnson syndrome;40例药物诱导的中毒性表皮坏死松解症的临床观察
2.Treatment with combination of corticosteroid with immunoglobulin in 15 patients with toxic epidermal necrolysis;糖皮质激素联合免疫球蛋白治疗中毒性表皮坏死松解症15例疗效观察
3)Toxic epidermal necrolysis中毒性表皮坏死松解症
1.Acute generalized exanthematous pustulosis mimicking toxic epidermal necrolysis;表现为中毒性表皮坏死松解症的急性泛发性发疹性脓疱病
2.Clinical analysis of 12 cases with toxic epidermal necrolysis;中毒性表皮坏死松解症12例临床分析
3.Analysis of 18 cases of major erythema multiforme and toxic epidermal necrolysis重症多形红斑及中毒性表皮坏死松解症18例临床分析
4)epidermolytic palmoplantar keratoderma表皮松解性掌跖角化症
1.Present status of the molecular genetics in epidermolytic palmoplantar keratoderma;表皮松解性掌跖角化症的分子遗传学研究进展
5)epidermolysis bullosa大疱性表皮松解症
1.One Case Report of Epidermolysis Bullosa先天性大疱性表皮松解症1例
6)bullous epidermal necrolysis大疱性表皮坏死松解症
延伸阅读
获得性大疱性表皮松解症 以张力性大疱为基本损害的一种皮肤病。又名真皮松解性类天疱疮。1970年代后从先天性大疱性表皮松解症中分出来，并命名。特点是发病年龄多在40岁以上。尼科利斯基氏征阴性，皮疹好发于四肢远端。大疱的出现常以轻微外伤为诱因。愈后常留下瘢痕和粟丘疹。组织病理学检查为表皮下疱,疱内可见红细胞,疱下有嗜中性细胞为主的炎症细胞浸润。疱周皮肤直接免疫荧光检查显示基底膜带有线状 IgG沉积。免疫电镜则显示免疫球蛋白沉积于基底膜的致密板下带。本病的诊断标准为：①表皮下大疱；②无家族发病史；③病程慢性；④基底膜带线状IgG沉着,用1MNaCl分离正常人皮肤为底物,以间接免疫荧光法，可见荧光带在分离皮肤的真皮侧，这也是与大疱性类天疱疮主要鉴别点。本病无特效治疗方法，避免外伤为重要措施。皮疹较广泛者，必要时可应用皮质类固醇激素如泼尼松。预后良好。
